Fat embolism syndrome in a child with dystonia musculorum deformans
نویسندگان
چکیده
منابع مشابه
Characterization of the rat mutant dystonic (dt): a new animal model of dystonia musculorum deformans.
An inherited neurological disorder characterized by sustained twisting movements during waking has been discovered in Sprague-Dawley rats. The mutation follows an autosomal recessive pattern of inheritance and has been named dystonic (dt). The rat mutants are indistinguishable from normal littermates in open field behavior and climbing activity prior to postnatal days 9 to 10. Clinical signs be...
متن کاملCharacteristic alterations in responses to imposed wrist displacements in parkinsonian rigidity and dystonia musculorum deformans.
The amplitude and temporal modulation of the segmented EMG activity in flexor carpi radialis, evoked by imposed angular wrist extension, was studied with respect to the level of pre-existing background activity in rigid parkinsonian (PK) and dystonia musculorum deformans (DMD) patients. The interdependence of the evoked M1 and M2-3 segments on pre-existing background EMG activity and initial ve...
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Fat embolism syndrome refers to a constellation of symptoms secondary to the presence of fat globules in the lung parenchyma and/or peripheral blood circulation. The syndrome is most often seen in association with long bone or pelvic fractures and can cause significant morbidity and mortality. The present randomized double blind placebo-controlled trial was conducted to evaluate the efficacy of...
متن کاملMotor Unit Abnormalities in Dystonia musculorum Mice
Dystonia musculorum (dt) is a mouse inherited sensory neuropathy caused by mutations in the dystonin gene. While the primary pathology lies in the sensory neurons of dt mice, the overt movement disorder suggests motor neurons may also be affected. Here, we report on the contribution of motor neurons to the pathology in dt(27J) mice. Phenotypic dt(27J) mice display reduced alpha motor neuron cel...
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A 76-yr-old-man with a right femoral neck fracture was scheduled to undergo bipolar hip arthroplasty during general anesthesia. The patient has been under appropriate medication for hepatitis C, hypertension, and diabetes mellitus. We prepared the patient for general anesthesia with minimum monitoring devices for noninvasive blood pressure, blood oxygen saturation, end-tidal carbon dioxide, ele...
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ژورنال
عنوان ژورنال: Case Reports
سال: 2012
ISSN: 1757-790X
DOI: 10.1136/bcr.12.2011.5466